Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment

Hereditary spherocytosis must always be suspected in children with anemia, hyperbilirubinemia, splenomegaly or cholelithiasis, in the asymptomatic individual with an affected relative, and in the neonate with hyperbilirubinemia with no blood group incompatibility; its early detection is key to avoid...

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Autores principales:	Donato, H., Crisp, R.L., Rapetti, M.C., García, E., Attie, M.
Formato:	JOUR
Materias:	Cholelithiasis Hemolytic anemia Hereditary spherocytosis Hyperbilirubinemia Splenectomy antibiotic therapy aplastic crisis cholelithiasis early diagnosis follow up hereditary spherocytosis human outcome assessment prophylaxis quality of life Review splenectomy symptomatology adolescent child complication preschool child Spherocytosis, Hereditary treatment outcome Adolescent Child Child, Preschool Humans Treatment Outcome
Acceso en línea:	http://hdl.handle.net/20.500.12110/paper_03250075_v113_n2_p168_Donato
Aporte de:	Biblioteca Digital - Facultad de Ciencias Exactas y Naturales (UBA) de Universidad de Buenos Aires

id	todo:paper_03250075_v113_n2_p168_Donato
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spelling	todo:paper_03250075_v113_n2_p168_Donato2023-10-03T15:23:15Z Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment Donato, H. Crisp, R.L. Rapetti, M.C. García, E. Attie, M. Cholelithiasis Hemolytic anemia Hereditary spherocytosis Hyperbilirubinemia Splenectomy antibiotic therapy aplastic crisis cholelithiasis early diagnosis follow up hereditary spherocytosis human outcome assessment prophylaxis quality of life Review splenectomy symptomatology adolescent child complication preschool child Spherocytosis, Hereditary treatment outcome Adolescent Child Child, Preschool Humans Spherocytosis, Hereditary Splenectomy Treatment Outcome Hereditary spherocytosis must always be suspected in children with anemia, hyperbilirubinemia, splenomegaly or cholelithiasis, in the asymptomatic individual with an affected relative, and in the neonate with hyperbilirubinemia with no blood group incompatibility; its early detection is key to avoid kernicterus. Follow-up of these patients is based on periodical control and supply of information on the adequate management of hemolytic or aplastic crisis, and early detection of cholelithiasis. The decision to perform splenectomy is usually associated with quality of life rather than life-threatening risk, and it should result from a consensus between patient, parents and physicians. The postsplenectomy follow-up is based on control of compliance with the prophylactic antibiotic therapy and the early diagnosis of infectious disorders. © 2015, Sociedad Argentina de Pediatria. All rights reserved. JOUR info:eu-repo/semantics/openAccess http://creativecommons.org/licenses/by/2.5/ar http://hdl.handle.net/20.500.12110/paper_03250075_v113_n2_p168_Donato
institution	Universidad de Buenos Aires
institution_str	I-28
repository_str	R-134
collection	Biblioteca Digital - Facultad de Ciencias Exactas y Naturales (UBA)
topic	Cholelithiasis Hemolytic anemia Hereditary spherocytosis Hyperbilirubinemia Splenectomy antibiotic therapy aplastic crisis cholelithiasis early diagnosis follow up hereditary spherocytosis human outcome assessment prophylaxis quality of life Review splenectomy symptomatology adolescent child complication preschool child Spherocytosis, Hereditary treatment outcome Adolescent Child Child, Preschool Humans Spherocytosis, Hereditary Splenectomy Treatment Outcome
spellingShingle	Cholelithiasis Hemolytic anemia Hereditary spherocytosis Hyperbilirubinemia Splenectomy antibiotic therapy aplastic crisis cholelithiasis early diagnosis follow up hereditary spherocytosis human outcome assessment prophylaxis quality of life Review splenectomy symptomatology adolescent child complication preschool child Spherocytosis, Hereditary treatment outcome Adolescent Child Child, Preschool Humans Spherocytosis, Hereditary Splenectomy Treatment Outcome Donato, H. Crisp, R.L. Rapetti, M.C. García, E. Attie, M. Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment
topic_facet	Cholelithiasis Hemolytic anemia Hereditary spherocytosis Hyperbilirubinemia Splenectomy antibiotic therapy aplastic crisis cholelithiasis early diagnosis follow up hereditary spherocytosis human outcome assessment prophylaxis quality of life Review splenectomy symptomatology adolescent child complication preschool child Spherocytosis, Hereditary treatment outcome Adolescent Child Child, Preschool Humans Spherocytosis, Hereditary Splenectomy Treatment Outcome
description	Hereditary spherocytosis must always be suspected in children with anemia, hyperbilirubinemia, splenomegaly or cholelithiasis, in the asymptomatic individual with an affected relative, and in the neonate with hyperbilirubinemia with no blood group incompatibility; its early detection is key to avoid kernicterus. Follow-up of these patients is based on periodical control and supply of information on the adequate management of hemolytic or aplastic crisis, and early detection of cholelithiasis. The decision to perform splenectomy is usually associated with quality of life rather than life-threatening risk, and it should result from a consensus between patient, parents and physicians. The postsplenectomy follow-up is based on control of compliance with the prophylactic antibiotic therapy and the early diagnosis of infectious disorders. © 2015, Sociedad Argentina de Pediatria. All rights reserved.
format	JOUR
author	Donato, H. Crisp, R.L. Rapetti, M.C. García, E. Attie, M.
author_facet	Donato, H. Crisp, R.L. Rapetti, M.C. García, E. Attie, M.
author_sort	Donato, H.
title	Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment
title_short	Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment
title_full	Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment
title_fullStr	Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment
title_full_unstemmed	Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment
title_sort	hereditary spherocytosis. review. part ii. symptomatology, outcome, complications, and treatment
url	http://hdl.handle.net/20.500.12110/paper_03250075_v113_n2_p168_Donato
work_keys_str_mv	AT donatoh hereditaryspherocytosisreviewpartiisymptomatologyoutcomecomplicationsandtreatment AT crisprl hereditaryspherocytosisreviewpartiisymptomatologyoutcomecomplicationsandtreatment AT rapettimc hereditaryspherocytosisreviewpartiisymptomatologyoutcomecomplicationsandtreatment AT garciae hereditaryspherocytosisreviewpartiisymptomatologyoutcomecomplicationsandtreatment AT attiem hereditaryspherocytosisreviewpartiisymptomatologyoutcomecomplicationsandtreatment
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Hereditary Spherocytosis. Review. Part II. Symptomatology, outcome, complications, and treatment

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