Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype
Background/Objective Data on IgG4-related disease (IgG4-RD) come almost exclusively from cohorts from Asia, Europe, and North America. We conducted this study to describe the clinical presentation, phenotype distribution, and association with sex, ethnicity, and serological markers in a large cohort...
Guardado en:
| Autores principales: | , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , |
|---|---|
| Formato: | Artículo |
| Lenguaje: | Español |
| Publicado: |
Lippincott Williams and Wilkins
2022
|
| Materias: | |
| Acceso en línea: | http://pa.bibdigital.ucc.edu.ar/3334/1/Mart%C3%ADn-Nares_Baenas_Cuellar.pdf |
| Aporte de: |
| id |
I38-R144-3334 |
|---|---|
| record_format |
dspace |
| institution |
Universidad Católica de Córdoba |
| institution_str |
I-38 |
| repository_str |
R-144 |
| collection |
Producción Académica Universidad Católica de Córdoba (UCCor) |
| language |
Español |
| orig_language_str_mv |
spa |
| topic |
R Medicina (General) |
| spellingShingle |
R Medicina (General) Martín-Nares, Eduardo Baenas, Diego Federico Cuellar Gutiérrez, María Carolina Hernández-Molina, Gabriela Ortiz, Alberto Christian Neira, Oscar Gutiérrez, Miguel A. Calvo, Romina Saad, Emanuel José Elgueta Pinochet, Sergio Gallo, Jesica Herrera Moya, Alejandra Mansilla Aravena, Bellanides Agustina Crespo Espíndola, María Elena Cairoli, Ernesto Bertoli, Ana María Córdoba, Mercedes Wurmann Kiblisky, Pamela Basualdo Arancibia, Washington Javier Badilla Piñeiro, María Natalia Gobbi, Carla Andrea Berbotto, Guillermo Ariel Pisoni, Cecilia N. Juárez, Vicente Cosatti, Micaela Ana Aste, Nora María Airoldi, Carla Llanos, Carolina Vergara Melian, Cristian Fabián Erlij Opazo, Daniel Goecke, Annelise Pastenes Montaño, Paula Andrea Tate, Patricio Pirola, Juan Pablo Stange Núñez, Lilith Burgos, Paula I. Mezzano Robinson, María Verónica Michalland H, Susana Silva Labra, Francisco Labarca Solar, Cristián Humberto Lencina, María Verónica Izquierdo Loaiza, Jorge Hernán Del Castillo Gil, David Julián Caeiro, Francisco Paira, Sergio Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype |
| topic_facet |
R Medicina (General) |
| description |
Background/Objective Data on IgG4-related disease (IgG4-RD) come almost exclusively from cohorts from Asia, Europe, and North America. We conducted this study to describe the clinical presentation, phenotype distribution, and association with sex, ethnicity, and serological markers in a large cohort of Latin American patients with IgG4-RD. Methods We performed a multicenter medical records review study including 184 Latin American IgG4-RD patients. We assigned patients to clinical phenotypes: group 1 (pancreato-hepato-biliary), group 2 (retroperitoneal/aortic), group 3 (head and neck-limited), group 4 (Mikulicz/systemic), and group 5 (undefined). We focused the analysis on how sex, ethnicity, and clinical phenotype may influence the clinical and serological presentation. Results The mean age was 50.8 ± 15 years. Men and women were equally affected (52.2% vs 48.8%). Fifty-four patients (29.3%) were assigned to group 1, 21 (11.4%) to group 2, 57 (30.9%) to group 3, 32 (17.4%) to group 4, and 20 (10.8%) to group 5. Male sex was associated with biliary tract (odds ratio [OR], 3.4; 95% confidence interval [CI], 1.36-8.26), kidney (OR, 3.4; 95% CI, 1.28-9.25), and retroperitoneal involvement (OR, 5.3; 95% CI, 1.45-20). Amerindian patients presented more frequently with atopy history and gallbladder involvement. Group 3 had a female predominance. Conclusions Latin American patients with IgG4-RD were younger, and men and women were equally affected compared with White and Asian cohorts. They belonged more commonly to group 1 and group 3. Retroperitoneal and aortic involvement was infrequent. Clinical and serological features differed according to sex, ethnicity, and clinical phenotype. |
| format |
Artículo |
| author |
Martín-Nares, Eduardo Baenas, Diego Federico Cuellar Gutiérrez, María Carolina Hernández-Molina, Gabriela Ortiz, Alberto Christian Neira, Oscar Gutiérrez, Miguel A. Calvo, Romina Saad, Emanuel José Elgueta Pinochet, Sergio Gallo, Jesica Herrera Moya, Alejandra Mansilla Aravena, Bellanides Agustina Crespo Espíndola, María Elena Cairoli, Ernesto Bertoli, Ana María Córdoba, Mercedes Wurmann Kiblisky, Pamela Basualdo Arancibia, Washington Javier Badilla Piñeiro, María Natalia Gobbi, Carla Andrea Berbotto, Guillermo Ariel Pisoni, Cecilia N. Juárez, Vicente Cosatti, Micaela Ana Aste, Nora María Airoldi, Carla Llanos, Carolina Vergara Melian, Cristian Fabián Erlij Opazo, Daniel Goecke, Annelise Pastenes Montaño, Paula Andrea Tate, Patricio Pirola, Juan Pablo Stange Núñez, Lilith Burgos, Paula I. Mezzano Robinson, María Verónica Michalland H, Susana Silva Labra, Francisco Labarca Solar, Cristián Humberto Lencina, María Verónica Izquierdo Loaiza, Jorge Hernán Del Castillo Gil, David Julián Caeiro, Francisco Paira, Sergio |
| author_facet |
Martín-Nares, Eduardo Baenas, Diego Federico Cuellar Gutiérrez, María Carolina Hernández-Molina, Gabriela Ortiz, Alberto Christian Neira, Oscar Gutiérrez, Miguel A. Calvo, Romina Saad, Emanuel José Elgueta Pinochet, Sergio Gallo, Jesica Herrera Moya, Alejandra Mansilla Aravena, Bellanides Agustina Crespo Espíndola, María Elena Cairoli, Ernesto Bertoli, Ana María Córdoba, Mercedes Wurmann Kiblisky, Pamela Basualdo Arancibia, Washington Javier Badilla Piñeiro, María Natalia Gobbi, Carla Andrea Berbotto, Guillermo Ariel Pisoni, Cecilia N. Juárez, Vicente Cosatti, Micaela Ana Aste, Nora María Airoldi, Carla Llanos, Carolina Vergara Melian, Cristian Fabián Erlij Opazo, Daniel Goecke, Annelise Pastenes Montaño, Paula Andrea Tate, Patricio Pirola, Juan Pablo Stange Núñez, Lilith Burgos, Paula I. Mezzano Robinson, María Verónica Michalland H, Susana Silva Labra, Francisco Labarca Solar, Cristián Humberto Lencina, María Verónica Izquierdo Loaiza, Jorge Hernán Del Castillo Gil, David Julián Caeiro, Francisco Paira, Sergio |
| author_sort |
Martín-Nares, Eduardo |
| title |
Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype |
| title_short |
Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype |
| title_full |
Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype |
| title_fullStr |
Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype |
| title_full_unstemmed |
Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype |
| title_sort |
clinical and serological features in latin american igg4-related disease patients differ according to sex, ethnicity, and clinical phenotype |
| publisher |
Lippincott Williams and Wilkins |
| publishDate |
2022 |
| url |
http://pa.bibdigital.ucc.edu.ar/3334/1/Mart%C3%ADn-Nares_Baenas_Cuellar.pdf |
| work_keys_str_mv |
AT martinnareseduardo clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT baenasdiegofederico clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT cuellargutierrezmariacarolina clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT hernandezmolinagabriela clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT ortizalbertochristian clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT neiraoscar clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT gutierrezmiguela clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT calvoromina clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT saademanueljose clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT elguetapinochetsergio clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT gallojesica clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT herreramoyaalejandra clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT mansillaaravenabellanidesagustina clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT crespoespindolamariaelena clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT cairoliernesto clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT bertolianamaria clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT cordobamercedes clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT wurmannkibliskypamela clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT basualdoarancibiawashingtonjavier clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT badillapineiromarianatalia clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT gobbicarlaandrea clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT berbottoguillermoariel clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT pisonicecilian clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT juarezvicente clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT cosattimicaelaana clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT astenoramaria clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT airoldicarla clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT llanoscarolina clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT vergarameliancristianfabian clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT erlijopazodaniel clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT goeckeannelise clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT pastenesmontanopaulaandrea clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT tatepatricio clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT pirolajuanpablo clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT stangenunezlilith clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT burgospaulai clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT mezzanorobinsonmariaveronica clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT michallandhsusana clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT silvalabrafrancisco clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT labarcasolarcristianhumberto clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT lencinamariaveronica clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT izquierdoloaizajorgehernan clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT delcastillogildavidjulian clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT caeirofrancisco clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype AT pairasergio clinicalandserologicalfeaturesinlatinamericanigg4relateddiseasepatientsdifferaccordingtosexethnicityandclinicalphenotype |
| _version_ |
1832592342202187776 |
| spelling |
I38-R144-33342025-04-11T18:12:53Z http://pa.bibdigital.ucc.edu.ar/3334/ Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype Martín-Nares, Eduardo Baenas, Diego Federico Cuellar Gutiérrez, María Carolina Hernández-Molina, Gabriela Ortiz, Alberto Christian Neira, Oscar Gutiérrez, Miguel A. Calvo, Romina Saad, Emanuel José Elgueta Pinochet, Sergio Gallo, Jesica Herrera Moya, Alejandra Mansilla Aravena, Bellanides Agustina Crespo Espíndola, María Elena Cairoli, Ernesto Bertoli, Ana María Córdoba, Mercedes Wurmann Kiblisky, Pamela Basualdo Arancibia, Washington Javier Badilla Piñeiro, María Natalia Gobbi, Carla Andrea Berbotto, Guillermo Ariel Pisoni, Cecilia N. Juárez, Vicente Cosatti, Micaela Ana Aste, Nora María Airoldi, Carla Llanos, Carolina Vergara Melian, Cristian Fabián Erlij Opazo, Daniel Goecke, Annelise Pastenes Montaño, Paula Andrea Tate, Patricio Pirola, Juan Pablo Stange Núñez, Lilith Burgos, Paula I. Mezzano Robinson, María Verónica Michalland H, Susana Silva Labra, Francisco Labarca Solar, Cristián Humberto Lencina, María Verónica Izquierdo Loaiza, Jorge Hernán Del Castillo Gil, David Julián Caeiro, Francisco Paira, Sergio R Medicina (General) Background/Objective Data on IgG4-related disease (IgG4-RD) come almost exclusively from cohorts from Asia, Europe, and North America. We conducted this study to describe the clinical presentation, phenotype distribution, and association with sex, ethnicity, and serological markers in a large cohort of Latin American patients with IgG4-RD. Methods We performed a multicenter medical records review study including 184 Latin American IgG4-RD patients. We assigned patients to clinical phenotypes: group 1 (pancreato-hepato-biliary), group 2 (retroperitoneal/aortic), group 3 (head and neck-limited), group 4 (Mikulicz/systemic), and group 5 (undefined). We focused the analysis on how sex, ethnicity, and clinical phenotype may influence the clinical and serological presentation. Results The mean age was 50.8 ± 15 years. Men and women were equally affected (52.2% vs 48.8%). Fifty-four patients (29.3%) were assigned to group 1, 21 (11.4%) to group 2, 57 (30.9%) to group 3, 32 (17.4%) to group 4, and 20 (10.8%) to group 5. Male sex was associated with biliary tract (odds ratio [OR], 3.4; 95% confidence interval [CI], 1.36-8.26), kidney (OR, 3.4; 95% CI, 1.28-9.25), and retroperitoneal involvement (OR, 5.3; 95% CI, 1.45-20). Amerindian patients presented more frequently with atopy history and gallbladder involvement. Group 3 had a female predominance. Conclusions Latin American patients with IgG4-RD were younger, and men and women were equally affected compared with White and Asian cohorts. They belonged more commonly to group 1 and group 3. Retroperitoneal and aortic involvement was infrequent. Clinical and serological features differed according to sex, ethnicity, and clinical phenotype. Lippincott Williams and Wilkins 2022 info:eu-repo/semantics/article info:eu-repo/semantics/closedAccess application/pdf spa http://pa.bibdigital.ucc.edu.ar/3334/1/Mart%C3%ADn-Nares_Baenas_Cuellar.pdf Martín-Nares, Eduardo, Baenas, Diego Federico, Cuellar Gutiérrez, María Carolina, Hernández-Molina, Gabriela, Ortiz, Alberto Christian, Neira, Oscar, Gutiérrez, Miguel A., Calvo, Romina, Saad, Emanuel José, Elgueta Pinochet, Sergio, Gallo, Jesica, Herrera Moya, Alejandra, Mansilla Aravena, Bellanides Agustina, Crespo Espíndola, María Elena, Cairoli, Ernesto ORCID: https://orcid.org/0000-0003-3210-3824 <https://orcid.org/0000-0003-3210-3824>, Bertoli, Ana María ORCID: https://orcid.org/0000-0002-9335-075X <https://orcid.org/0000-0002-9335-075X>, Córdoba, Mercedes, Wurmann Kiblisky, Pamela, Basualdo Arancibia, Washington Javier, Badilla Piñeiro, María Natalia, Gobbi, Carla Andrea, Berbotto, Guillermo Ariel, Pisoni, Cecilia N., Juárez, Vicente, Cosatti, Micaela Ana, Aste, Nora María, Airoldi, Carla, Llanos, Carolina, Vergara Melian, Cristian Fabián, Erlij Opazo, Daniel, Goecke, Annelise, Pastenes Montaño, Paula Andrea, Tate, Patricio, Pirola, Juan Pablo, Stange Núñez, Lilith, Burgos, Paula I., Mezzano Robinson, María Verónica, Michalland H, Susana, Silva Labra, Francisco, Labarca Solar, Cristián Humberto, Lencina, María Verónica, Izquierdo Loaiza, Jorge Hernán, Del Castillo Gil, David Julián, Caeiro, Francisco and Paira, Sergio (2022) Clinical and Serological Features in Latin American IgG4-Related Disease Patients Differ According to Sex, Ethnicity, and Clinical Phenotype. Journal of Clinical Rheumatology, 28 (6). pp. 285-292. ISSN 1076-1608 https://journals.lww.com/jclinrheum/Abstract/2022/09000/Clinical_and_Serological_Features_in_Latin.1.aspx info:eu-repo/semantics/altIdentifier/doi/10.1097/RHU.0000000000001858 |