Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature

Desmoid-type fibromatosis (DF) is a rare monoclonal, fibroblastic proliferation characterized by an unpredictable and variable clinical course. We present the case of a 56-year-old woman who underwent total thyroidectomy for papillary thyroid carcinoma in 2012 and who developed a cervical mass at th...

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Detalles Bibliográficos
Autores principales: Ramírez Stieben, Luis Agustín, Pozzi, Daniel
Formato: Artículo revista
Lenguaje:Inglés
Publicado: Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2023
Materias:
Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/40408
Aporte de:
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institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-327
container_title_str Revista de la Facultad de Ciencias Médicas de Córdoba
language Inglés
format Artículo revista
topic papillary thyroid carcinoma
desmoid
Gardner syndrome
cáncer papilar tiroideo
desmoide
síndrome de Gardner
câncer papilífero da tireoide
desmoide
síndrome de Gardner
spellingShingle papillary thyroid carcinoma
desmoid
Gardner syndrome
cáncer papilar tiroideo
desmoide
síndrome de Gardner
câncer papilífero da tireoide
desmoide
síndrome de Gardner
Ramírez Stieben, Luis Agustín
Pozzi, Daniel
Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature
topic_facet papillary thyroid carcinoma
desmoid
Gardner syndrome
cáncer papilar tiroideo
desmoide
síndrome de Gardner
câncer papilífero da tireoide
desmoide
síndrome de Gardner
author Ramírez Stieben, Luis Agustín
Pozzi, Daniel
author_facet Ramírez Stieben, Luis Agustín
Pozzi, Daniel
author_sort Ramírez Stieben, Luis Agustín
title Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature
title_short Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature
title_full Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature
title_fullStr Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature
title_full_unstemmed Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature
title_sort papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature
description Desmoid-type fibromatosis (DF) is a rare monoclonal, fibroblastic proliferation characterized by an unpredictable and variable clinical course. We present the case of a 56-year-old woman who underwent total thyroidectomy for papillary thyroid carcinoma in 2012 and who developed a cervical mass at the left laterocervical level during follow-up, raising the diagnosis of tumor recurrence. Computed tomography of the neck showed solid formations with heterogeneous contrast uptake in the right lateral region of the neck. At the level of the thoracic operculum, a second 26-mm formation was observed that medially contacted the left lateral wall of the trachea. Lateral lymphadenectomy was performed, which was incomplete. Histology showed findings consistent with desmoid-type fibromatosis. DF are slowly proliferating, non-metastatic tumors with a highly invasive capacity that are usually present in familial adenomatous polyposis (FAP)-Gardner syndrome. Our case had a history of massive colonic polyposis and first-degree relatives of colorectal cancer.
publisher Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2023
url https://revistas.unc.edu.ar/index.php/med/article/view/40408
work_keys_str_mv AT ramirezstiebenluisagustin papillarythyroidcarcinomawithdesmoidfibromatosisacasereportandreviewofliterature
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AT ramirezstiebenluisagustin carcinomapapilardetiroidesconfibromatosisdesmoidereportedecasoyrevisiondelaliteratura
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first_indexed 2024-09-03T21:04:25Z
last_indexed 2024-09-03T21:04:25Z
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spelling I10-R327-article-404082023-12-01T19:41:10Z Papillary thyroid carcinoma with desmoid fibromatosis: a case report and review of literature Carcinoma papilar de tiroides con fibromatosis desmoide: reporte de caso y revisión de la literatura Carcinoma papilífero de tireoide com fibromatose desmóide: relato de caso e revisão da literatura Ramírez Stieben, Luis Agustín Pozzi, Daniel papillary thyroid carcinoma desmoid Gardner syndrome cáncer papilar tiroideo desmoide síndrome de Gardner câncer papilífero da tireoide desmoide síndrome de Gardner Desmoid-type fibromatosis (DF) is a rare monoclonal, fibroblastic proliferation characterized by an unpredictable and variable clinical course. We present the case of a 56-year-old woman who underwent total thyroidectomy for papillary thyroid carcinoma in 2012 and who developed a cervical mass at the left laterocervical level during follow-up, raising the diagnosis of tumor recurrence. Computed tomography of the neck showed solid formations with heterogeneous contrast uptake in the right lateral region of the neck. At the level of the thoracic operculum, a second 26-mm formation was observed that medially contacted the left lateral wall of the trachea. Lateral lymphadenectomy was performed, which was incomplete. Histology showed findings consistent with desmoid-type fibromatosis. DF are slowly proliferating, non-metastatic tumors with a highly invasive capacity that are usually present in familial adenomatous polyposis (FAP)-Gardner syndrome. Our case had a history of massive colonic polyposis and first-degree relatives of colorectal cancer. La fibromatosis de tipo desmoide (FD) es una rara proliferación fibroblástica monoclonal caracterizada por un curso clínico impredecible y variable. Presentamos el caso de una mujer de 56 años intervenida de tiroidectomía total por carcinoma papilar de tiroides en 2012 y que durante el seguimiento desarrolla una masa cervical a nivel laterocervical izquierdo, planteando el diagnóstico de recidiva tumoral. La tomografía computarizada de cuello demostró formaciones sólidas con captación heterogénea de contraste en la región lateral derecha del cuello. A nivel del opérculo torácico se observó una segunda formación de 26 mm que contactaba medialmente con la pared lateral izquierda de la tráquea. Se realizó una linfadenectomía lateral, que resultó incompleta. La histología mostró hallazgos compatibles con FD. La FD son tumores de proliferación lenta, no metastásicos y con una capacidad altamente invasiva que suelen estar presentes en la poliposis adenomatosa familiar (PAF)-síndrome de Gardner. Nuestro caso tenía antecedentes de poliposis colónica masiva y familiares de primer grado de cáncer colorrectal. A fibromatose desmóide (FD) é uma rara proliferação fibroblástica monoclonal caracterizada por um curso clínico imprevisível e variável. Apresentamos o caso de uma mulher de 56 anos que foi submetida a tireoidectomia total por carcinoma papilífero de tireoide em 2012 e que desenvolveu uma massa cervical em nível laterocervical esquerdo durante o acompanhamento, levando ao diagnóstico de recidiva tumoral. A tomografia computadorizada do pescoço demonstrou formações sólidas com realce heterogêneo pelo meio de contraste na região lateral direita do pescoço. Ao nível do desfiladeiro torácico, observou-se uma segunda formação de 26 mm que contatava medialmente a parede lateral esquerda da traqueia. Foi realizada linfadenectomia lateral, que foi incompleta. A histologia mostrou achados compatíveis com FD. Os FD são tumores não metastáticos, de proliferação lenta, com capacidade altamente invasiva, que geralmente estão presentes na síndrome de Gardner da polipose adenomatosa familiar (PAF). Nosso caso tinha história de polipose colônica maciça e um parente de primeiro grau com câncer colorretal. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2023-09-29 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion Text application/pdf text/html https://revistas.unc.edu.ar/index.php/med/article/view/40408 10.31053/1853.0605.v80.n3.40408 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 80 No. 3 (2023); 289-300 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 80 Núm. 3 (2023); 289-300 Revista da Faculdade de Ciências Médicas de Córdoba; v. 80 n. 3 (2023); 289-300 1853-0605 0014-6722 10.31053/1853.0605.v80.n3 eng https://revistas.unc.edu.ar/index.php/med/article/view/40408/42637 https://revistas.unc.edu.ar/index.php/med/article/view/40408/42650 Derechos de autor 2023 Universidad Nacional de Córdoba http://creativecommons.org/licenses/by-nc/4.0