Primary neuroendocrine tumor of the common bile duct
Primary neuroendocrine tumors (NETs) of the bile duct are extremely rare and represent only 0.2-2% of all gastrointestinal NETs. Within the biliary system, the main bile duct is the most affected site. A 28-year-old man with a 6-month history of intermittent jaundice, pruritus, and choluria. MRCP, P...
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| Autores principales: | , , , , , , |
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| Formato: | Artículo revista |
| Lenguaje: | Español |
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Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2023
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| Materias: | |
| Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/40368 |
| Aporte de: |
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I10-R327-article-40368 |
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ojs |
| institution |
Universidad Nacional de Córdoba |
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I-10 |
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R-327 |
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Revista de la Facultad de Ciencias Médicas de Córdoba |
| language |
Español |
| format |
Artículo revista |
| topic |
bile duct neoplasms neuroendocrine tumors Anti-Ki67 neoplasias de la vía biliar tumores neuroendocrinos antígeno Ki-67 neoplasias do ducto biliar tumores neuroendócrinos antígeno Ki-67 |
| spellingShingle |
bile duct neoplasms neuroendocrine tumors Anti-Ki67 neoplasias de la vía biliar tumores neuroendocrinos antígeno Ki-67 neoplasias do ducto biliar tumores neuroendócrinos antígeno Ki-67 Gasque, Rodrigo Antonio Zaietta, Noelia Del Bueno, María Luján Saenz, Julieta Chahdi Beltrame, Magalí Quiñonez, Emilio Gastón Mattera, Francisco Juan Primary neuroendocrine tumor of the common bile duct |
| topic_facet |
bile duct neoplasms neuroendocrine tumors Anti-Ki67 neoplasias de la vía biliar tumores neuroendocrinos antígeno Ki-67 neoplasias do ducto biliar tumores neuroendócrinos antígeno Ki-67 |
| author |
Gasque, Rodrigo Antonio Zaietta, Noelia Del Bueno, María Luján Saenz, Julieta Chahdi Beltrame, Magalí Quiñonez, Emilio Gastón Mattera, Francisco Juan |
| author_facet |
Gasque, Rodrigo Antonio Zaietta, Noelia Del Bueno, María Luján Saenz, Julieta Chahdi Beltrame, Magalí Quiñonez, Emilio Gastón Mattera, Francisco Juan |
| author_sort |
Gasque, Rodrigo Antonio |
| title |
Primary neuroendocrine tumor of the common bile duct |
| title_short |
Primary neuroendocrine tumor of the common bile duct |
| title_full |
Primary neuroendocrine tumor of the common bile duct |
| title_fullStr |
Primary neuroendocrine tumor of the common bile duct |
| title_full_unstemmed |
Primary neuroendocrine tumor of the common bile duct |
| title_sort |
primary neuroendocrine tumor of the common bile duct |
| description |
Primary neuroendocrine tumors (NETs) of the bile duct are extremely rare and represent only 0.2-2% of all gastrointestinal NETs. Within the biliary system, the main bile duct is the most affected site. A 28-year-old man with a 6-month history of intermittent jaundice, pruritus, and choluria. MRCP, PET-CT and endoscopic ultrasound were performed. A well-differentiated neuroendocrine neoplasia was diagnosed. Complete resection of the main bile duct was performed with lymphadenectomy of the hepatic pedicle with Roux-en-Y hepaticojejunostomy, without complications. The patient had an adequate evolution and nowadays he’s disease-free. Primary neuroendocrine tumors of the bile duct are extremely rare. They may present clinically and radiologically similar to perihilar cholangiocarcinoma, which makes preoperative diagnosis difficult. Radical resection is indicated. Usually, they are well differentiated tumors, being the Ki-67 labeling index a reliable prognostic marker. |
| publisher |
Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
| publishDate |
2023 |
| url |
https://revistas.unc.edu.ar/index.php/med/article/view/40368 |
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2024-09-03T21:04:24Z |
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I10-R327-article-403682023-07-10T12:07:38Z Primary neuroendocrine tumor of the common bile duct Tumor neuroendocrino primario del conducto hepático común Tumor neuroendócrino primário do ducto hepático comum Gasque, Rodrigo Antonio Zaietta, Noelia Del Bueno, María Luján Saenz, Julieta Chahdi Beltrame, Magalí Quiñonez, Emilio Gastón Mattera, Francisco Juan bile duct neoplasms neuroendocrine tumors Anti-Ki67 neoplasias de la vía biliar tumores neuroendocrinos antígeno Ki-67 neoplasias do ducto biliar tumores neuroendócrinos antígeno Ki-67 Primary neuroendocrine tumors (NETs) of the bile duct are extremely rare and represent only 0.2-2% of all gastrointestinal NETs. Within the biliary system, the main bile duct is the most affected site. A 28-year-old man with a 6-month history of intermittent jaundice, pruritus, and choluria. MRCP, PET-CT and endoscopic ultrasound were performed. A well-differentiated neuroendocrine neoplasia was diagnosed. Complete resection of the main bile duct was performed with lymphadenectomy of the hepatic pedicle with Roux-en-Y hepaticojejunostomy, without complications. The patient had an adequate evolution and nowadays he’s disease-free. Primary neuroendocrine tumors of the bile duct are extremely rare. They may present clinically and radiologically similar to perihilar cholangiocarcinoma, which makes preoperative diagnosis difficult. Radical resection is indicated. Usually, they are well differentiated tumors, being the Ki-67 labeling index a reliable prognostic marker. Los tumores neuroendocrinos (TNE) primarios de la vía biliar son extremadamente raros y representan sólo el 0.2-2% de todos los TNE gastrointestinales. Dentro del sistema biliar, la vía biliar principal es el sitio más afectado. Hombre de 28 años con cuadro de 6 meses de evolución caracterizado por ictericia intermitente, prurito y coluria. Se realizó colangiopancreatoresonancia magnética nuclear, PET-TC y ultrasonido endoscópico que concluyeron neoplasia neuroendocrina bien diferenciada. Se realizó resección completa de la vía biliar principal con linfadenectomía del pedículo hepático con hepaticoyeyunoanastomosis en Y de Roux, sin complicaciones. El paciente cursó adecuada evolución y se encuentra libre de enfermedad. Los tumores neuroendocrinos primarios de la vía biliar son extremadamente raros, presentándose clínica y radiológicamente como lesiones similares al colangiocarcinoma perihiliar lo que dificulta el diagnóstico preoperatorio. Está indicado su tratamiento quirúrgico radical. Suelen ser bien diferenciados, siendo el antígeno Ki-67 un marcador pronóstico confiable. Tumores neuroendócrinos primários (TNEs) do ducto biliar são extremamente raros e representam apenas 0,2-2% de todos os TNEs gastrointestinais. Dentro do sistema biliar, o ducto biliar principal é o local mais afetado. Homem de 28 anos com história de 6 meses caracterizada por icterícia intermitente, prurido e colúria. Foram realizadas ressonância magnética colangiopancreatonuclear, PET-CT e ultrassonografia endoscópica, que concluíram neoplasia neuroendócrina bem diferenciada. Foi realizada ressecção completa da via biliar principal com linfadenectomia do pedículo hepático com hepatojejunoanastomose em Y de Roux, sem intercorrências. A paciente teve evolução adequada e encontra-se livre da doença. Os tumores neuroendócrinos primários da via biliar são extremamente raros, apresentando-se clínica e radiologicamente como lesões semelhantes ao colangiocarcinoma peri-hilar, o que dificulta o diagnóstico pré-operatório. Seu tratamento cirúrgico radical está indicado. Geralmente são bem diferenciados, sendo o antígeno Ki-67 um marcador prognóstico confiável. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2023-06-30 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion Text Texto Texto application/pdf text/html https://revistas.unc.edu.ar/index.php/med/article/view/40368 10.31053/1853.0605.v80.n2.40368 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 80 No. 2 (2023); 141-144 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 80 Núm. 2 (2023); 141-144 Revista da Faculdade de Ciências Médicas de Córdoba; v. 80 n. 2 (2023); 141-144 1853-0605 0014-6722 10.31053/1853.0605.v80.n2 spa https://revistas.unc.edu.ar/index.php/med/article/view/40368/41731 https://revistas.unc.edu.ar/index.php/med/article/view/40368/41192 Derechos de autor 2023 Universidad Nacional de Córdoba http://creativecommons.org/licenses/by-nc/4.0 |