Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature
Introduction: Congenital renal arteriovenous fistula is an abnormal connection between the arterial and venous system. Since the first case described in 1928 by Varela et al, no more than 200 cases have been published. Material and Method: A 45-year-old woman consulted for severe abdominal and low-b...
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Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2020
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Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/29743 |
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I10-R10-article-29743 |
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Universidad Nacional de Córdoba |
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Revistas de la UNC |
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Español |
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Artículo revista |
topic |
arteriovenous fistula arteriovenous malformations abdomen acute congenital abnormalities fistula arteriovenosa malformacion arteriovenosa abdomen agudo anomalias congenitas fístula arteriovenosa malformações arteriovenosas abdome agudo anormalidades congênitas |
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arteriovenous fistula arteriovenous malformations abdomen acute congenital abnormalities fistula arteriovenosa malformacion arteriovenosa abdomen agudo anomalias congenitas fístula arteriovenosa malformações arteriovenosas abdome agudo anormalidades congênitas Palacios Huatuco, Rene Manuel Pantoja Pachajoa, Diana Alejandra Pinsak, Agustin Ezequiel Mandojana, Facundo Ignacio Doniquian, Alejandro Marcelo Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature |
topic_facet |
arteriovenous fistula arteriovenous malformations abdomen acute congenital abnormalities fistula arteriovenosa malformacion arteriovenosa abdomen agudo anomalias congenitas fístula arteriovenosa malformações arteriovenosas abdome agudo anormalidades congênitas |
author |
Palacios Huatuco, Rene Manuel Pantoja Pachajoa, Diana Alejandra Pinsak, Agustin Ezequiel Mandojana, Facundo Ignacio Doniquian, Alejandro Marcelo |
author_facet |
Palacios Huatuco, Rene Manuel Pantoja Pachajoa, Diana Alejandra Pinsak, Agustin Ezequiel Mandojana, Facundo Ignacio Doniquian, Alejandro Marcelo |
author_sort |
Palacios Huatuco, Rene Manuel |
title |
Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature |
title_short |
Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature |
title_full |
Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature |
title_fullStr |
Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature |
title_full_unstemmed |
Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature |
title_sort |
congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature |
description |
Introduction: Congenital renal arteriovenous fistula is an abnormal connection between the arterial and venous system. Since the first case described in 1928 by Varela et al, no more than 200 cases have been published.
Material and Method: A 45-year-old woman consulted for severe abdominal and low-back pain associated with arterial hypertension. The CT scan showed an infrarenal retroperitoneal lesion with invasion of neighboring structures.
Results: During the abdominal exploration, a vascular-looking lesion of 60 x 34 x 41 mm was identified. It was associated with right nephrectomy.
Discussion: The etiology of congenital fistulas remains unknown; it is believed that a congenital arterial aneurysm erodes into an adjacent vein and gradually increases its size. Other authors believe that the fistula exists since birth and gradually increases its size until it causes symptoms.
Conclusion: Congenital arteriovenous fistulas are rare entities, representing less than 25% of all renal arteriovenous malformations. |
publisher |
Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
publishDate |
2020 |
url |
https://revistas.unc.edu.ar/index.php/med/article/view/29743 |
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first_indexed |
2022-08-20T01:27:32Z |
last_indexed |
2022-08-20T01:27:32Z |
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I10-R10-article-297432021-07-15T20:12:32Z Congenital renal arteriovenous fistula: a rare cause of acute abdomen and a review of its literature Fístula arteriovenosa renal congénita: una causa rara de abdomen agudo y revisión de la literatura Fístula arteriovenosa renal congênita: uma causa rara de abdome agudo e revisão da literatura Palacios Huatuco, Rene Manuel Pantoja Pachajoa, Diana Alejandra Pinsak, Agustin Ezequiel Mandojana, Facundo Ignacio Doniquian, Alejandro Marcelo arteriovenous fistula arteriovenous malformations abdomen acute congenital abnormalities fistula arteriovenosa malformacion arteriovenosa abdomen agudo anomalias congenitas fístula arteriovenosa malformações arteriovenosas abdome agudo anormalidades congênitas Introduction: Congenital renal arteriovenous fistula is an abnormal connection between the arterial and venous system. Since the first case described in 1928 by Varela et al, no more than 200 cases have been published. Material and Method: A 45-year-old woman consulted for severe abdominal and low-back pain associated with arterial hypertension. The CT scan showed an infrarenal retroperitoneal lesion with invasion of neighboring structures. Results: During the abdominal exploration, a vascular-looking lesion of 60 x 34 x 41 mm was identified. It was associated with right nephrectomy. Discussion: The etiology of congenital fistulas remains unknown; it is believed that a congenital arterial aneurysm erodes into an adjacent vein and gradually increases its size. Other authors believe that the fistula exists since birth and gradually increases its size until it causes symptoms. Conclusion: Congenital arteriovenous fistulas are rare entities, representing less than 25% of all renal arteriovenous malformations. Introducción: La fístula arteriovenosa renal congénita es una conexión anómala entre el sistema arterial y venoso. Desde el primer caso descrito en 1928 por Varela y cols, no más de 200 casos han sido publicados. Material y Método: Mujer de 45 años consultó por dolor abdominal y lumbar severo, asociado a hipertensión arterial. En tomografía computada se observó lesión retroperitoneal infrarrenal con invasión de estructuras vecinas. Resultados: En exploración abdominal se identificó lesión de aspecto vascular de 60 x 34 x 41 mm. Se asoció a nefrectomía derecha. Discusión: La etiología de las fístulas congénitas sigue siendo desconocida, se cree que un aneurisma arterial congénito erosiona hacia una vena adyacente y aumenta su tamaño lentamente. Otros autores creen que la fístula existe desde el nacimiento e incrementa progresivamente de tamaño hasta producir síntomas. Conclusión: Las fístulas arteriovenosas congénitas son entidades raras, representando menos del 25% del total de las malformaciones arteriovenosas renales. Introdução: A fístula arteriovenosa renal congênita é uma conexão anômala entre o sistema arterial e o venoso. Desde o primeiro caso descrito em 1928 por Varela et. al., menos de 200 casos foram publicados. Material e Método: Mulher de 45 anos consultou por dor abdominal e lombar severa, associada a hipertensão arterial. Na tomografia computadorizada, foi observada lesão retroperitonial infrarrenal com invasão de estruturas vizinhas. Resultados: Na exploração abdominal foi identificada lesão de aspecto vascular de 60 x 34 x 41 mm. Foi associada a nefrectomia direita. Discussão: A etiologia das fístulas congênitas continua sendo desconhecida, acredita-se que um aneurisma arterial congênito provoca erosão em direção a uma veia adjacente e aumenta seu tamanho lentamente. Outros autores acreditam que a fístula existe desde o nascimento e incrementa progressivamente de tamanho até produzir sintomas. Conclusão: As fístulas arteriovenosas congênitas são entidades raras, representando menos de 25% do total das malformações arteriovenosas renais. Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2020-12-19 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf text/html https://revistas.unc.edu.ar/index.php/med/article/view/29743 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 77 No. 4 (2020); 356-359 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 77 Núm. 4 (2020); 356-359 Revista da Faculdade de Ciências Médicas de Córdoba; v. 77 n. 4 (2020); 356-359 1853-0605 0014-6722 10.31053/1853.0605.v77.n4 spa https://revistas.unc.edu.ar/index.php/med/article/view/29743/32388 https://revistas.unc.edu.ar/index.php/med/article/view/29743/32439 Derechos de autor 2020 Universidad Nacional de Córdoba http://creativecommons.org/licenses/by-nc/4.0 |